Abstract :
We hereby, present a female with Kartagener’s syndrome associated with mixed connective tissue disorder. Kartagener’s syndrome is a rare congenital malformation comprising triad of sinusitis, situs inversus and bronchiectasis. Mixed connective tissue disorder is an autoimmune disorder comprising of scleroderma, systemic lupus erythematous, myositis and presence of antibody to riboneucleoprotein called U1-RNP.
Keyword :
Bronchiectasis; Kartagener’s Syndrome; Mixed connective tissue disorder; Usual interstitial pneumonitis