Abstract :
Sex cord tumor with annular tubules (SCTAT) accounts for approximately 2.3% of Sex cord stromal tumor (SCST) and is a relatively infrequently encountered, distinctive type of ovarian neoplasm. SCTAT is most commonly seen in females of reproductive age group. Peutz-Jeghers syndrome (PJS) may be associated with SCTAT in one-third of the patients. A 23 year old unmarried female presented with pain abdomen and mass per abdomen. Ultrasonography revealed a left adnexal mass. Considering clinical presentation and radiological findings, a differential diagnosis of teratoma/ dysgerminoma was given. Intraoperatively, a large left ovarian mass was noted. The mass was excised and sent for histopathology study. On microscopy,
diagnosis of SCTAT was rendered. SCTAT are uncommon tumors with unique morphologic pattern. Our case was a non-syndromic case with no other features of PJS. Since 15-20% of non-syndromic cases can have a malignant course later in life, a long term follow up is required.
Key message: Ovarian tumors at young age like SCTAT are very important to diagnose accurately as patient’s prognosis has to be weighed against preserving fertility and these tumors should be followed up for a long period.
Keyword :
Ovarian tumor, Peutz-Jeghers syndrome, Reproductive age group.