Abstract :
We report the case of an 18-year-old female presenting with a 5-month history of fever, progressive limb weakness, and generalized swelling. Initially diagnosed with Guillain-Barré syndrome (GBS), the patient’s clinical course evolved into chronic inflammatory demyelinating polyneuropathy (CIDP). Further investigation, including serological testing and a lip biopsy, revealed positive autoimmune markers (anti-SSA (Ro) and anti-SSB (La)) and confirmed the diagnosis of Sjögren’s syndrome-associated autoimmune neuropathy. The patient was managed with intravenous steroids, antibiotics, diuretics, and physiotherapy, resulting in substantial clinical improvement. This case underscores the importance of a thorough diagnostic approach and individualized treatment strategies in managing autoimmune-related neuropathies.
Keyword :
Case report, Sjögren's syndrome, Pediatric Sjögren's syndrome, Guillain-Barré syndrome, Chronic inflammatory demyelinating polyneuropathy, Autoimmune neuropathy, Plasmapheresis, Autoimmune diseases.