Abstract :
Raynaud’s syndrome indicates reversible, intermittent pallor or cyanosis or both, frequently affect fingers or toes, less often can affect the nose, ears, lips, nipples, or knees in response to cold or stress and is rare in childhood. Raynaud’s phenomenon (RP) is an extremely unusual finding in early newborn. In severe cases the ischemia may lead to areas of infarction in hands and feet. In this case we describe a one-day old male early newborn who presented with unilateral acrocyanosis over the tip of fingers of the
right hand since birth. He was healthy otherwise. Although acrocyanosis in newborn is known to be a benign and self-limiting condition, typically. It is bilateral and symmetric with no other symptoms. The unilateral acrocyanosis was an atypical finding in this newborn. After the exclusion of all other diseases by investigations, he was diagnosed to have primary RD. Due to the rarity of RD in children, we have reviewed the pathophysiology, epidemiology and management of RD and also discuss the differential diagnosis of unilateral and bilateral acrocyanosis in newborn.
Keyword :
Primary Raynaud’s disease, Unilateral atypical.