Abstract :
Mirror movement is a rare neurologic soft sign associated with many conditions. Dyke-Davidoff- Masson syndrome (DDMS) is a rare condition characterized by unilateral cerebral atrophy and facial asymmetry, hemiparesis, seizures and mental retardation. Association of mirror movements with DDMS which was previously suggested in a few studies, will be presented and discussed. We report a case of 10 year old male with infantile right hemiparesis now presented with 5 year history of mirror movements of both upper limbs. There is right hemiatrophy with spastic right hemiparesis. MRI brain revealed hemiatrophy of left hemisphere, left half of midbrain with thickening of left skull vault with normal cervical spine, features consistent with DDMS. Although treatment of both conditions is conservative, goal of treatment is improving the quality of life of the patient so that with existing limitation, patient can lead more meaningful life
Keyword :
Mirror movement, Dyke-Davidoff-Masson Syndrome, Hemiatrophy