Abstract :
Congenital Cystic Adenomatoid malformation consists of hamartomatosis or Dysplastic lung tissue mixed with more normal lung, generally confined to one lobe. This congenital pulmonary disorder occurs in 1:25,000-1:35,000 births. These lesions arise from excessive disorganised proliferation of Bronchial structures and probably results from an embryologic insult before 35thday of gestation. CCAM can be diagnosed in Utero by Ultrasonography; the median age for the diagnosis is usually 21 weeks of gestation. Patient can present in the neonatal period with significant respiratory distress, recurrent respiratory infections and pneumothorax. Patient with smaller lesions are usually asymptomatic until mid-childhood, when it can present with episodes of Recurrent or persistent pulmonary infections or chest pain.
Keyword :
Congenital Cystic Adenomatoid Malformation (CCAM), Infant, premature, Infant, low birth weight