Abstract :
Klippel feil syndrome is a rare skeletal disorder primarily characterized by abnormal union or fusion of
two or more cervical vertebrae which is often associated with cervical canal stenosis. This results in a short
neck, a low hairline at the back of the head, a limited range of motion in the neck and infrequently an
atlanto- axial instability.
Here we report a case of type 3 paediatric Klippel Feil syndrome who underwent Sprengel deformity repair
in prone position and its anesthetic implications.
A careful assessment of airway and an algorithmic approach towards management is needed in children
with KFS. The various spine deformities associated with KFS demand careful positioning and a
reconfirmation of appropriate ETT position, airway pressures and lung compliance is recommended in
these children.
Keyword :
Klippel Feil syndrome, Paediatric, Airway management, Prone positioning, Difficult airway.