Peripheral primitive neuroectodermal tumor of the upper limb: A case report and review of literature


Article PDF :

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Article type :

Case Report

Author :

Sarah Afzal, Alen Thomas, Osamah Rahman Khan

Volume :

3

Issue :

1

Abstract :

Peripheral Primitive Neuroectodermal Tumors (pPNET) are rare malignant tumors characterized by small round cells of neuroectodermal origin. They usually occur between the age of 6-25 years, mostly in soft tissues or bones and belong to the Ewing Sarcoma Family of Tumors (ESFT). We report an unusual case of pPNET of the upper extremity in a 24-year-old male. The purpose of reporting this case is it being a rare diagnosis which demands early detection and treatment as the presence or absence of metastasis is the most significant prognostic factor.