Abstract :
Dyschromatosis universalis hereditaria (DUH) is a pigmentary disorder of rare occurence comprising both hyperpigmented and hypopigmented macules forming an irregular pattern. Although ocular albinism, iris coloboma, aniridia, chorioretinal coloboma have been associated with it, we report a case of DUH with bilateral keratopathy which is a rare co-existence. This case represents the rarest association of DUH with decompensated cornea which was managed successfully with penetrating keratoplasty.
Keyword :
Dyschromatosis, Keratopathy, Keratoplasty.