Von Recklinghausen\\\'s disease intra oral manifestation: A rare entity


Article PDF :

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Article type :

Case Report

Author :

Kundoor Vinay Kumar Reddy, Kotya Naik Maloth, Tejaswini Meesala, Moni Thakur

Volume :

4

Issue :

3

Abstract :

Neurofibromatosis (NF) is an autosomal-dominant disorder, characterized by neurocutaneous tumors arising within multiple organs, which the diagnosis is made based on clinical criteria proposed by National Institute of Health Consensus Development Conference. Neurofibromatosis type I (NF-1), also termed as von Recklinghausen’s disease, is the most common type accounting 90% of the cases. We report a clinical case of NF-1 with oral manifestations in a 60-year-old female patient.

Keyword :

Glioma, Lisch nodules, Neurofibromatosis, Neurocutaneous tumors.