Tuberous sclerosis complex: A case report and literature review


Article PDF :

Veiw Full Text PDF

Article type :

Review Article

Author :

Amjad Ali, Dipankar Das, Harsha Bhattacharjee, Damaris Magdalene, Divakant Misra

Volume :

4

Issue :

3

Abstract :

Tuberous Sclerosis Complex is a rare genetic disorder of autosomal dominant inheritance. It is a neurocutaneous syndrome exhibiting multiple hamartomatous proliferations involving multiple organ system such as brain, kidney, heart, lungs, eyes and skin. Here, we present a case report of a 7year old male patient with characteristic clinical and radiological features of Tuberosis Sclerosis Complex.

Keyword :

Genetic disorder, Multiple hamartomas, Neurocutaneous syndrome, Tuberous sclerosis complex.