Abstract :
Incontinentia pigmenti (IP) is an X linked dominant genodermatosis that affects skin, eyes, CNS, teeth and skeletal system. Skin manifestations are most common and occur in four quite distinctive phases. Here, we present a female neonate with vesiculobullous lesions in the limbs and trunk which healed with hyperpigmentation. Skin biopsy revealed eosinophilic spongiosis and suprabasal bullae, suggestive of incontinentia pigmenti.
Keyword :
Incontinentia pigmenti, vesiculobullous lesion, Genodermatosis.