Volume :
3
Issue :
3
Abstract :
Patients of neurofibromatosis sometimes develop neuroendocrine tumour [NET]. These NETs are usually found in duodenum or periampullary region .We report a case of a patient with neurofibromatosis, who presented with obstructive jaundice. Upper gastrointestinal (UGI) endoscopy showed a periampullary growth. An endoscopic biopsy was taken which was not conclusive of any neoplastic growth. A pylorus preserving pancreaticoduodenectomy was performed. The specimen was sent for histopathology. The tumor was later on diagnosed as well differentiated NET, low grade.